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Pulmonary-renal syndrome

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Revision as of 14:43, 12 December 2023 by Aidan (talk | contribs)
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Background

  • Usually refers to a combination of glomerulonephritis and pulmonary hemorrhage
  • Most common causes are ANCA-associated vaculitis and anti-GBM disease

Differential Diagnosis

  • ANCA-associated small vessel vaculitis (70%)
    • Granulomatosis with polyangiitis
    • Eosinophilic granulomatosis with polyangiitis
    • Microscopic polyangiitis
  • Anti-GBM antibody disease (Goodpasture syndrome) (20%)
  • Rarely
    • Cryoglobulinemic vasculitis
    • Systemic lupus erythematosus
    • IgA vasculitis
  • Even more rare: thrombotic microangiopathy, rheumatoid arthritis, systemic sclerosis, mixed connective tissue disease, polymyositis, and dermatomyositis
Retrieved from "https://idwiki.org/index.php?title=Pulmonary-renal_syndrome&oldid=10305"
Categories:
  • Respirology
  • Nephrology
  • Rheumatology
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This page was last edited on 12 December 2023, at 14:43.
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