IgG4 disease

From IDWiki
(Redirected from IgG4-related disease)

Organ Involvement

  • Pancreas: autoimmune pancreatitis
  • Bile ducts: IgG4-associated cholangitis
  • Salivary gland
    • Chronic sclerosing sialadenitis (Küttner's tumour)
    • IgG4-related plasmacytic exocrinopathy (Mikulicz's disease)
  • Chest
    • Patchy ground-glass, nodular, and consolidative opacities
    • Mediastinal fibrosis and adenopathy
  • Retroperitoneum
    • Chronic periaortitis
    • Idiopathic retroperitoneal fibrosis
  • Kidneys: tubulointerstitial nephritis
  • Orbits: IgG4-associated pseudolymphoma
  • Inflammatory bowel disease: ulcerative colitis