Hepatopulmonary syndrome
From IDWiki
Definition
- Syndrome characterized by liver disease, intrapulmonary vascular dilatation, and abnormal oxygenation
- Even mild liver disease
- Separate from portopulmonary hypertension
Epidemiology
- 5-30% of patients with liver disease
Clinical Presentation
- Platypnea
- Orthodeoxia
- Clubbing
- Cyanosis
Investigations
Management
- Liver transplant is the only cure
