Superficial siderosis

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Revision as of 13:15, 25 August 2024 by Aidan (talk | contribs) (Created page with "== Background == * Chronic condition caused by recurrent or persistent bleeding into the subarachnoid space, which causes hemosiderin deposits * Slowly progressive neurodegenerative condition * Classified into cortical or infratentorial == Clinical Manifestations == * Average time from onset to diagnosis is 1 to 10 years * Initially presents with sensorineural hearing loss and slowly progressive cerebellar ataxia * The classic triad, which is uncommon, including heari...")
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Background

  • Chronic condition caused by recurrent or persistent bleeding into the subarachnoid space, which causes hemosiderin deposits
  • Slowly progressive neurodegenerative condition
  • Classified into cortical or infratentorial

Clinical Manifestations

  • Average time from onset to diagnosis is 1 to 10 years
  • Initially presents with sensorineural hearing loss and slowly progressive cerebellar ataxia
  • The classic triad, which is uncommon, including hearing loss, ataxia, and myelopathy
  • Symptoms progress chronically and slowly