Moya moya syndrome
From IDWiki
Definition
- Chronic progressive stroke syndrome caused by bilateral carotid occlusion
Differential Diagnosis
For the radiographic appearance of moya moya
- Primary moya moya syndrome
- Atherosclerosis
- Cranial irradiation
- Pediatric diseases
- Down/Turner/Alagille syndromes
- Sickle cell disease
- Neurofibromatosis type 1
- Tuberous sclerosis
- Sturge-Weber syndrome
- Metabolic disorders
- Gongenital heart disease
- Infections
- Meningitis
- Other viral or bacterial infections
- Hematologic disorders
- Sick cell disease
- Beta thalassemia
- Fanconi anemia
- Hereditary spherocytosis
- Homocystinuria and hyperhomocyteinemia
- Factor XI deficiency
- Essential thrombocythemia
- Autoimmune disease
- Systemic lupus erythematosus
- Polyarteritis nodosa
- Graves disease and thyroiditis
- Antiphospholipid antibody syndrome
- Type 1 diabetes
- Brain neoplasm
- Head trauma
Risk Factors
- Japanese and Asian population
- Family history
Management
- Antiplatelet therapy (e.g. aspirin)
- Revascularization
- EC-IC bypass
Prognosis
- Often die from intracranial hemorrhage
